KLIPPEL TRENAUNAY SYNDROME: SURGICAL TREATMENT OF VARICOSE VEINS
Keywords:
Kippel-Trenaunay-Weber Syndrome, ultrasonography, color doppler, surgical treatment, varicose veinsAbstract
Klippel-Trenaunay syndrome reflects severe venous hypertension and clinically consists oJ- large caliber varicose veins, capillary nevus and hypertrophy of tissues and bones of the affected limb. It is common, in patients with this diseases, the presence of edema, fibras is of skin, ocher dermatitis, ulcer and pain, symptoms of venous stasis that J,-equently incapacitate them to work. ln the absence of agenesis or hypoplasia of the deep venous system, which are frequently associated, surgical treatment should be considered for the varicose veins. After a thorough preoperatory evaluation and explanation of the risks and benefits of the surgical treatment, four patients were operated on. There was no significant postoperative complication, and there was a high inner satisfaction of the patients. Despite the small number of cases, it an he inferred that, for patients who meet the previously mentioned criterias, surgical treatm.ent of varicose veins in. individuais with Klippel-Trenaunay-Weber syndrome is possible and advisable.
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References
Arguedas MR, Shore G, Wilcox CM. Congenital vascular lesions ofthe gastrointestinal tract: blue rubber bleb nevus and Klippel-Trenaunay syndromes. South MedJ 2001; 94(4):405-10.
Baraldini V, Coletti M, Cipolat L, Santuari D, Vercellio G. Early surgi cal managementofKlippel-Trenaunay syndorme in childhood can prevent long-term haemodynamic effects of distal venous hypertension. J Pediatr Surg 2002; 3 7 (2) :232-5.
Capraro PA, Fischer J, Hammond DC, Grossman JA. Klippel-Trenaunay syndorme. Plast Reconstr Surg 2002; 109(6):2052-62.
Dervendizi Sikova D, Pavlova LT, V'lckova Laskoska MT, Nikolovska ST, Caca Biljanovska N. Naevus varicosus osteohypertrophicus: an early diagnostic approach. Adv Exp Med Biol 1999; 455:535-40.
Dimakakos PB, Portinos A. Regarding Surgical treatment of venous malformations in Klippel-Trenaunay syndrome. J Vasc Surg 2001; 34(3):573-4.
Duque JM, Munoz Navas M, Betes MT, Subtil JC, Angos R. Afectacion de colon en el sindrome de Klippel Trenaunay Weber. Colonic involvement in the Klippel-Trenaunay-Weber syndrome. Rev EspEnfermDig 2000; 92(1):44-5.
Fumess PD, BarqawiAZ, Bisignani G, Decter RM. Klippel-Trenaunay syndrome: 2 case reports and a review of genitourinary manifestations. J Urol 2001; (4)166: 1418-20.
Garteiz Martinez D, Robledo Ogazon F, Fuente Lira M, Mejia Hemandez MC, Blanco Benavides R. Rectorragia como complicacion del sindrome de Klippel-Trenaunay. Rectorrhagia as complication of Klippel-Trenaunay syndrome. Rev GastroenterolMex 1999; 64(4): 181-5.
Kato M, Chiba Y, Sakai K, Orikasa S. Endoscopic neodymium: yttrium aluminium gamet (Nd: Y AG) laser irradiation of a bladder hemangioma associated with Klippel-W eber syndrome. lnt J Urol 2000; 7(4):145-8.
Linge C, Prager TM. TMJ morphology and function in a patient with Klippel-Trenaunay syndrome: case report. J Orofac Orthop 2000; 61(3):217-21.
Mello NA. Síndromes vasculares. São Paulo: FundoBYK; 1999.
MorinJR,LeeJ, Yong R, Chagares W.Klippel-Trenaunay syndrome: an unsual presentation of unilateral leg edema. J Am Pediatr Med Assoe 2000; 90(8):421-4.
Muller-Lessmann V, Behrendt A, Wetzel WE, Petersen K, Anders D. Orofacial findings in the Kl i ppel--Trenaunay syndrome. Int J Pediatr Dent 2001; 11(3):225-9.
Noel AA, Gloviczki P, Cherry KJ, Rooke TW, Stanson A W, Driscoll DJ. Surgical treatment of venous malformations in Klippel-Trenaunay syndrome. J Vasc Surg 2000; 32(5):840-7.
Ozdiler E, Akcam MO, Sayin MO. Craniofacial characteristics of Klippel-Feil syndrome in an eight year old female. J Clin Pediatr Dent 2000 Spring; 24(3):249-54.
Sethi S, Shubha BS. Klippel-Trenaunay syndrome. IndianJ Pediatr 2001; 68(8):787-9.
ShekarrizB, Upadhyay J,SmithC,KazmersA,Frontera R. Massive hematuria in adults with Klippel-Trenaunay syndrome associated with vascular malformation of the bladder. Urol Int 2000; 64(4):226-8.
Thomsen M, Krübcr M, Schneider U, Carstens C. Congenital limb deficiences associated with Klippel-Feil syndorme: a survey of 57 subjects. Acta Orthop Scand 2000; 71(5):461-4.
Walder B, Kapelanski DP, Auger WR, Fedullo PF. Successful pulmonary thromboendarterectomy in a patient with Klippel-Trenaunay syndrome. Chest 2000; 117(5):1520-2.
Wilson CL, Song LM, Chua H, Ferrara M, Devine RM, Dozois RR, et ai. Bleeding from cavernous angiomatosis of the rectum in Klippel-Trenaunay syndrome: report of three cases and literature review. Am J Gastroenterol 2001; 96(9):2783-8.
