NEUROFIBROMATOSIS TYPE I WITH INTRAORAL MANIFESTATION
Keywords:
mouth, von Recklinghausen's diseases, neurofibroma, neurofibromatosisAbstract
Neurofibromatosis type I is the most common clinicai variant of a group of genetic disorders known as neurofibromatosis that primarily affects the ce/1 growth of neural tissues. The purpose of this work is to describe one case of a woman with neurofibromatosis type I presenting oral cavity involvement. The clinica/ signs of the patient fulfilled the National lnstitute of Health criteria for neurofibromatosis type I and the intraoral-nodular lesion was removed, analyzed microscopically, and after H&E staining and S-100 immunohistochemical assay, the diagnosis of neurofibroma was confirmed. After two months, this intraoral lesion recurred.
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