Pain evaluation in children and adolescents with sickle cell disease
Keywords:
Hemoglobin SC disease, Pain, Pain measurement, QuestionnairesAbstract
Objective
To eva[uate the frequency. intensity. location and duration of pain in patlents with síckle cell disease. monitored by the Pediatríc Hematology Unit, Department of Pediatrics af Universidade Federal de São Paulo (São Paulo - Brazil).
Methods
Patients with sickle cell disease were evaluated by means of home-based questionnaires given to the patients and parents/caregivers. For pain measurement
we used three scales: analog visual, faces and verbal.
Results
The study group comprised 23 patients (aged 8-15 years). Thirteen patients (56.5%) were male; 16 patients (70.0%) presented sickle cell anemia, 4 (17.0%)
had sickle cell SC disease and 3 (13.O%) suffered from sickle cell disease Beta*thalassemia. We observed pain related to sickle cell disease in 12 patients (52.2%). The average intensity of the worst pain (at home) and monthly average pain were 5.4 and 5.0 respectively; 9/12 patients (75.0%) presented pain in more than one location per event; 100.O% reported using pharmacological measures at home to alleviate the pain; pain had a greater impact on school activities and
leisure, The correlation. between the pain reported by the 23 patients and that reported by their respective caregivers, showed that the caregivers score was
significantly higher (Wilcoxon test, p=0.013), but we did not observe significant dívergence between them using the Kappa test (p=0.007).
Conclusion
Patients with sickle cell disease present moderate pain intensity between medical visits, with a negative impact on their daily activities.
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