Duchenne muscular dystrophy: respíratory complications and treatment

Authors

  • Jakeline Gordinho Fonseca
  • Marcella Jardim da Franca Machado
  • Cristiane Leal de Moraes e Silva Ferraz

Keywords:

Muscular dystrophy Duchenne, Respiratory insufficiency, Respiratory therapy

Abstract

Duchenne Muscular Dystrophy is a genetic disturbance found on the X chromosome that affects specially boys. lt is also a progressive and irreversible degeneration of the skeletal muscles that causes a general muscular debility, and the respiratory disorders are the principal cause of death. So, it is important to study the possible respiratory disorders that assai/ people with Duchenne Muscular Dystrophy, and the varied treatments used to reduce the morbidity and increase the patient's quality of life. The present artic/e was dane by using a bibliographic study of scientific articles, researched in the following databases (MedLine, Lilacs, Capes, Pubmed, SciELO), through key words like Duchenne Muscular Dystrophy, respiratory disorder and respiratory therapy. We verified that there are controversies regarding the practice of physica/ exercises, strength training and muscle resistance in the respiratory treatment. The appropriate treatment and caution can diminish the symptoms, improve the quality of life and reduce the high morbidity and early death of these patients.

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Published

2007-04-30

How to Cite

Fonseca, J. G., Machado, M. J. da F., & Ferraz, C. L. de M. e S. (2007). Duchenne muscular dystrophy: respíratory complications and treatment. Revista De Ciências Médicas, 16(2). Retrieved from https://seer.sis.puc-campinas.edu.br/cienciasmedicas/article/view/1067

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