Elastosis perforans serpiginosa
Keywords:
Hepatolenticular degeneration, Skin diseases, Penicillamine, Elastic tissueAbstract
Elastosis perforans serpiginosa is a rare reactive perforanting dermatosis characterized by a process of transepidermal elimination of elastic fibers. The cause is unknown, but a genetically determined defect of elastic tissue has been proposed. Commonly occur in young persons in the second decade, with a higher incidence among males. Clinically, umbilicated papules with a central plug appear characteristically on the neck, creating the elevated serpiginous border. It has been characterized in idiopathic, reactive (with associated connective tissue disease) and penicillamine-induced. Different options of treatment have been described in the literature. We describe a 47-year-old female with elastosis perforans serpiginosa and Wilson’s disease who has been treated with longterm penicillamine therapy.
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References
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